<?xml version="1.0" encoding="UTF-8"?><xml><records><record><source-app name="Biblio" version="7.x">Drupal-Biblio</source-app><ref-type>17</ref-type><contributors><authors><author><style face="normal" font="default" size="100%">Calatroni, Marta</style></author><author><style face="normal" font="default" size="100%">Oliva, Elena</style></author><author><style face="normal" font="default" size="100%">Gianfreda, Davide</style></author><author><style face="normal" font="default" size="100%">Gregorini, Gina</style></author><author><style face="normal" font="default" size="100%">Allinovi, Marco</style></author><author><style face="normal" font="default" size="100%">Ramirez, Giuseppe A</style></author><author><style face="normal" font="default" size="100%">Bozzolo, Enrica P</style></author><author><style face="normal" font="default" size="100%">Monti, Sara</style></author><author><style face="normal" font="default" size="100%">Bracaglia, Claudia</style></author><author><style face="normal" font="default" size="100%">Marucci, Giulia</style></author><author><style face="normal" font="default" size="100%">Bodria, Monica</style></author><author><style face="normal" font="default" size="100%">Sinico, Renato A</style></author><author><style face="normal" font="default" size="100%">Pieruzzi, Federico</style></author><author><style face="normal" font="default" size="100%">Moroni, Gabriella</style></author><author><style face="normal" font="default" size="100%">Pastore, Serena</style></author><author><style face="normal" font="default" size="100%">Emmi, Giacomo</style></author><author><style face="normal" font="default" size="100%">Esposito, Pasquale</style></author><author><style face="normal" font="default" size="100%">Catanoso, Mariagrazia</style></author><author><style face="normal" font="default" size="100%">Barbano, Giancarlo</style></author><author><style face="normal" font="default" size="100%">Bonanni, Alice</style></author><author><style face="normal" font="default" size="100%">Vaglio, Augusto</style></author></authors></contributors><titles><title><style face="normal" font="default" size="100%">ANCA-associated vasculitis in childhood: recent advances.</style></title><secondary-title><style face="normal" font="default" size="100%">Ital J Pediatr</style></secondary-title><alt-title><style face="normal" font="default" size="100%">Ital J Pediatr</style></alt-title></titles><keywords><keyword><style  face="normal" font="default" size="100%">Age Distribution</style></keyword><keyword><style  face="normal" font="default" size="100%">Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis</style></keyword><keyword><style  face="normal" font="default" size="100%">Antibodies, Antineutrophil Cytoplasmic</style></keyword><keyword><style  face="normal" font="default" size="100%">Child</style></keyword><keyword><style  face="normal" font="default" size="100%">Child, Preschool</style></keyword><keyword><style  face="normal" font="default" size="100%">Churg-Strauss Syndrome</style></keyword><keyword><style  face="normal" font="default" size="100%">Female</style></keyword><keyword><style  face="normal" font="default" size="100%">Granulomatosis with Polyangiitis</style></keyword><keyword><style  face="normal" font="default" size="100%">Humans</style></keyword><keyword><style  face="normal" font="default" size="100%">Incidence</style></keyword><keyword><style  face="normal" font="default" size="100%">Male</style></keyword><keyword><style  face="normal" font="default" size="100%">Microscopic Polyangiitis</style></keyword><keyword><style  face="normal" font="default" size="100%">Rare Diseases</style></keyword><keyword><style  face="normal" font="default" size="100%">Risk Assessment</style></keyword><keyword><style  face="normal" font="default" size="100%">Severity of Illness Index</style></keyword><keyword><style  face="normal" font="default" size="100%">Sex Distribution</style></keyword><keyword><style  face="normal" font="default" size="100%">Survival Rate</style></keyword></keywords><dates><year><style  face="normal" font="default" size="100%">2017</style></year><pub-dates><date><style  face="normal" font="default" size="100%">2017 May 05</style></date></pub-dates></dates><volume><style face="normal" font="default" size="100%">43</style></volume><pages><style face="normal" font="default" size="100%">46</style></pages><language><style face="normal" font="default" size="100%">eng</style></language><abstract><style face="normal" font="default" size="100%">&lt;p&gt;Anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitides are rare systemic diseases that usually occur in adulthood. They comprise granulomatosis with polyangiitis (GPA, Wegener's), microscopic polyangiitis (MPA) and eosinophilic granulomatosis with polyangiitis (EGPA, Churg-Strauss syndrome). Their clinical presentation is often heterogeneous, with frequent involvement of the respiratory tract, the kidney, the skin and the joints. ANCA-associated vasculitis is rare in childhood but North-American and European cohort studies performed during the last decade have clarified their phenotype, patterns of renal involvement and their prognostic implications, and outcome. Herein, we review the main clinical and therapeutic aspects of childhood-onset ANCA-associated vasculitis, and provide preliminary data on demographic characteristics and organ manifestations of an Italian multicentre cohort.&lt;/p&gt;</style></abstract><issue><style face="normal" font="default" size="100%">1</style></issue><custom1><style face="normal" font="default" size="100%">http://www.ncbi.nlm.nih.gov/pubmed/28476172?dopt=Abstract</style></custom1></record></records></xml>